Document Type

Article

Peer Reviewed

1

Publication Date

12-5-2016

NLM Title Abbreviation

Epilepsy Behav Case Rep

Journal/Book/Conference Title

Epilepsy & Behavior Case Reports

PubMed ID

28239546

DOI of Published Version

10.1016/j.ebcr.2016.11.003

Start Page

24

End Page

27

Total Pages

4

Abstract

A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was diagnosed with Rasmussen syndrome by pathology and promptly treated with functional hemispherotomy. Rasmussen syndrome is a rare progressive neurological disorder, the only definitive cure for which is hemispheric disconnection. The disease presents a management dilemma, especially early in disease course without characteristic neuroimaging features. A high index of suspicion, multidisciplinary approach, and clear timely communication with the family are critical.

Keywords

OAfund, Rasmussen's encephalitis, Rasmussen syndrome, Early diagnosis, Functional hemispherectomy, Peri-insular functional hemispherotomy

Journal Article Version

Version of Record

Published Article/Book Citation

Epilepsy & Behavior Case Reports 7 (2017) 24–27

https://doi.org/10.1016/j.ebcr.2016.11.003

Rights

Copyright (c) 2016 The Author(s)

Creative Commons License

Creative Commons License
This work is licensed under a Creative Commons Attribution-Noncommercial-No Derivative Works 4.0 License.

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URL

https://ir.uiowa.edu/neurosurgery_pubs/1