NLM Title Abbreviation
Epilepsy Behav Case Rep
Epilepsy & Behavior Case Reports
DOI of Published Version
A 7-year-old previously healthy girl presented with a left-sided focal seizure without impaired consciousness and subsequently developed epilepsia partialis continua. Initial MRI was normal, and the subsequent images only showed a focal T2/FLAIR hyperintense area without cortical atrophy. She was diagnosed with Rasmussen syndrome by pathology and promptly treated with functional hemispherotomy. Rasmussen syndrome is a rare progressive neurological disorder, the only definitive cure for which is hemispheric disconnection. The disease presents a management dilemma, especially early in disease course without characteristic neuroimaging features. A high index of suspicion, multidisciplinary approach, and clear timely communication with the family are critical.
OAfund, Rasmussen's encephalitis, Rasmussen syndrome, Early diagnosis, Functional hemispherectomy, Peri-insular functional hemispherotomy
Journal Article Version
Version of Record
Published Article/Book Citation
Epilepsy & Behavior Case Reports 7 (2017) 24–27
Copyright (c) 2016 The Author(s)
Creative Commons License
This work is licensed under a Creative Commons Attribution-Noncommercial-No Derivative Works 4.0 License.